A Rare Cause of Chylothorax in Children: Gorham-Stout Syndrome
نویسندگان
چکیده
منابع مشابه
Erratum: Pregnancy Complicated by Gorham–Stout Disease and Refractory Chylothorax
[This corrects the article DOI: 10.1055/s-0036-1593443.].
متن کاملPregnancy Complicated by Gorham–Stout Disease and Refractory Chylothorax
Introduction Gorham-Stout Disease (GSD) is a rare disorder of bony destruction due to lymphangiomatosis, and is often triggered by hormones. One complication of GSD is the development of chylothorax, which carries a high mortality rate. Very little experience has been published to guide management in GSD during pregnancy to optimize both fetal and maternal health. Case Study A 20-year-old woman...
متن کاملGorham-Stout syndrome: a case report.
Gorham-Stout syndrome, is an extremely rare disease of the bone, characterized for vascular and lymphatic channels proliferation in bony segments and consequent osseous resorption. There are around 200 cases reported around the world. Although bisphosphonates are used for symptoms relief, there is no standardized treatment established. We present a case that was diagnosed in our centre secondar...
متن کاملAn Unusual Cause of Recurrent Chylothorax: Gorham Syndrome
Gorham syndrome, which is also called diffuse lymphangiomatosis, is characterised by excessive osteolysis due to uncontrolled lymphatic or vascular proliferation involving bones, of unknown etiology. Chylothorax may accompany Gorham syndrome in case of invasion of lymphatic vessels, or thoracic duct due to neighboring affected ribs, scapula or vertebrae. Chylothorax and vertebral invasion is se...
متن کاملGorham-Stout syndrome of the shoulder
INTRODUCTION Gorham-Stout syndrome (GSS) is a rare but severe subtype of idiopathic osteolysis. There are no guidelines for the treatment of GSS. We analysed different diagnostic and therapeutic regimes and we describe the sucessful treatment of GSS considering individual patient factors. METHODS We diagnosed three patients with shoulder-specific GSS using clinical, radiological and histopath...
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ژورنال
عنوان ژورنال: Turkish Journal of Pediatric Disease
سال: 2018
ISSN: 1307-4490,2148-3566
DOI: 10.12956/tjpd.2018.375